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Primary immunodeficiency diseasesdef...
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Aghamohammadi, Asghar.
Primary immunodeficiency diseasesdefinition, diagnosis, and management /
紀錄類型:
書目-電子資源 : Monograph/item
正題名/作者:
Primary immunodeficiency diseasesedited by Nima Rezaei, Asghar Aghamohammadi, Luigi D. Notarangelo.
其他題名:
definition, diagnosis, and management /
其他作者:
Rezaei, Nima.
出版者:
Berlin, Heidelberg :Springer Berlin Heidelberg :2017.
面頁冊數:
xvii, 582 p. :ill., digital ;24 cm.
Contained By:
Springer eBooks
標題:
Immunological deficiency syndromes.
電子資源:
http://dx.doi.org/10.1007/978-3-662-52909-6
ISBN:
9783662529096$q(electronic bk.)
Primary immunodeficiency diseasesdefinition, diagnosis, and management /
Primary immunodeficiency diseases
definition, diagnosis, and management /[electronic resource] :edited by Nima Rezaei, Asghar Aghamohammadi, Luigi D. Notarangelo. - 2nd ed. - Berlin, Heidelberg :Springer Berlin Heidelberg :2017. - xvii, 582 p. :ill., digital ;24 cm.
Introduction on Primary Immunodeficiency Diseases -- Combined T- and B-Cell Immunodeficiencies -- Predominantly Antibody Deficiencies -- Phagocytes Defects -- Genetic Disorders of Immune Regulation -- Defects in Intrinsic and Innate Immunity: Receptors and Signaling Components -- Autoinflammatory Disorders -- Complement Deficiencies -- Other Well-Defined Immunodeficiencies -- Syndromic Immunodeficiencies.
Primary immunodeficiency diseases (PIDs) are a group of inborn disorders of the immune system, characterized by increased susceptibility to infections, autoimmunity, and cancers. Although PIDs were previously considered rare conditions, the number of diagnosed cases is growing rapidly, and about 300 different forms of PIDs have already been recognized. Nevertheless, because of inadequate medical awareness, misdiagnosis or late diagnosis occurs in a significant number of patients, leading to avoidable morbidity and mortality. The first edition of this practical reference textbook was widely welcomed by scientists and clinicians from around the world. This new edition has been extensively revised to reflect advances in knowledge and includes various PIDs not previously covered. For each disease, information is provided on definition, etiology, clinical manifestations, diagnosis, and management. Every effort has been made to ensure that, throughout, the text is easy to read and readily comprehensible. The book will represent an ideal resource for specialists when engaging in diagnosis, clinical decision-making, and treatment planning. It will also prove invaluable for doctors in training and other physicians and nurses who wish to learn more about PIDs.
ISBN: 9783662529096$q(electronic bk.)
Standard No.: 10.1007/978-3-662-52909-6doiSubjects--Topical Terms:
277790
Immunological deficiency syndromes.
LC Class. No.: RC606 / .P747 2017
Dewey Class. No.: 616.979
Primary immunodeficiency diseasesdefinition, diagnosis, and management /
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Introduction on Primary Immunodeficiency Diseases -- Combined T- and B-Cell Immunodeficiencies -- Predominantly Antibody Deficiencies -- Phagocytes Defects -- Genetic Disorders of Immune Regulation -- Defects in Intrinsic and Innate Immunity: Receptors and Signaling Components -- Autoinflammatory Disorders -- Complement Deficiencies -- Other Well-Defined Immunodeficiencies -- Syndromic Immunodeficiencies.
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Primary immunodeficiency diseases (PIDs) are a group of inborn disorders of the immune system, characterized by increased susceptibility to infections, autoimmunity, and cancers. Although PIDs were previously considered rare conditions, the number of diagnosed cases is growing rapidly, and about 300 different forms of PIDs have already been recognized. Nevertheless, because of inadequate medical awareness, misdiagnosis or late diagnosis occurs in a significant number of patients, leading to avoidable morbidity and mortality. The first edition of this practical reference textbook was widely welcomed by scientists and clinicians from around the world. This new edition has been extensively revised to reflect advances in knowledge and includes various PIDs not previously covered. For each disease, information is provided on definition, etiology, clinical manifestations, diagnosis, and management. Every effort has been made to ensure that, throughout, the text is easy to read and readily comprehensible. The book will represent an ideal resource for specialists when engaging in diagnosis, clinical decision-making, and treatment planning. It will also prove invaluable for doctors in training and other physicians and nurses who wish to learn more about PIDs.
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